SC Perinatal/infantile-onset HPP 2 mg/kg tds wkly or 1 mg/kg 6 times wkly. May be increased to up to 3 mg/kg tds wkly for lack of efficacy (eg, no improvement in resp status, growth or radiographic findings).
Juvenile-onset HPP 2 mg/kg tds wkly or 1 mg/kg 6 times wkly.